Phenylketonuria (PKU) is an inborn error of amino acid metabolism,
characterized by persistent hyperphenylalaninemia. There is no cure for PKU, however,
early diagnosis and treatment during the first month of life, make it possible to prevent
all the mentioned consequences. The treatment of classic and moderate PKU is
nutritional, based on a diet restricted in Phe, and supplemented with special formulas
free of Phe. The chapter is handling phenylketonuria (PKU) overview, highflying the
treatment strategies, incidence, nutrition, and PKU Diet, and development and
innovation of food for PKU including some home recipes.
Keywords: Foods for phenylketonuric, Hyperphenylalaninemia diet, Nutrition
and PKU, PKU food development.
